MSCTA在肺动脉分支起源异常及合并畸形中的应用价值OA
Application value of MSCTA in pulmonary artery branch origin anomalies and associated malformations
目的:探讨MSCTA在诊断肺动脉分支起源异常及合并畸形中的应用价值.方法:回顾性收集2018年5月—2025年11月于我院经手术或DSA证实为肺动脉分支起源异常患者的MSCTA图像及三维后处理图像,分析MSCTA诊断肺动脉分支起源异常及合并畸形的准确性.结果:共纳入46例肺动脉分支起源异常患者,其中一侧肺动脉起源于升主动脉13例(右肺动脉11例、左肺动脉2例),近端型(靠近主动脉瓣)11例(84.6%);肺动脉吊带13例;一侧肺动脉缺如20例.手术或DSA证实82.3%(38/46)的患者合并其他畸形,共110处.最常合并的心内畸形是房间隔缺损(ASD)38处(34.5%),最常合并的血管畸形是动脉导管未闭(PDA)19处(17.3%),合并肺发育不良7处(6.4%),合并支气管狭窄6处(5.5%),合并支气管发育变异1处(2.6%),发现1例罕见的贝里综合征.MSCTA对肺动脉分支起源异常的总检出率为93.5%(43/46),诊断合并心血管畸形的准确率为92.7%(102/110),漏误诊肺动脉开口与其他血管相近及合并的微小心内畸形.结论:肺动脉分支起源异常是一类罕见的先天性疾病,通常合并ASD、PDA、肺发育不良等其他畸形,MSCTA有助于提供精确的解剖学描述,并识别相关的异常,为临床制定治疗方案提供关键影像学依据.
Objective:To explore the application value of MSCTA in the diagnosis of abnormal origin of pulmonary artery and associated malformations.Methods:A retrospective study was conducted on 46 patients with abnormal origin of pulmonary artery confirmed by surgery or DSA in our hospital from May 2018 to November 2025.Their MSCTA images and three-dimensional post-processing images were collected,and the diagnostic accuracy of MSCTA for abnormal origin of pulmonary artery and associated malformations was analyzed.Results:Among the 46 patients,13 had unilateral pulmonary artery originating from the ascending aorta(11 right,2 left),with 84.6%(11/13)being the proximal type(near the aortic valve);13 had pulmonary artery sling,and 20 had unilateral pulmonary artery agenesis.Surgery or DSA confirmed 82.3%(38/46)of patients had 110 associated malformations.The most common intracardiac malformation was atrial septal defect(ASD,38,34.5%),and the most common vascular malformation was patent ductus arteriosus(PDA,19,17.3%).Other associated malfor‑mations included pulmonary hypoplasia(7,6.4%),tracheal stenosis(6,5.5%),bronchial developmental variation(1,2.6%),and 1 case of rare Berry syndrome.The overall detection rate of abnormal origin of pulmonary artery by MSCTA was 93.5%(43/46),and the diagnostic accuracy for associated cardiovascular malformations was 92.7%(102/110).Missed or misdiagnosed cases were mainly those with pulmonary artery ostium adjacent to other vessels or tiny intracardiac malformations.Conclu-sion:abnormal origin of pulmonary artery is a rare congenital disease,often accompanied by ASD,PDA,pulmonary hypopla‑sia and other malformations.MSCTA can provide accurate anatomical descriptions and identify related abnormalities,which provides key imaging evidence for clinical treatment planning.
赵细辉;崔学龙;黄昀;马海彦;许梓;王荣品
贵州省精准影像诊疗国际科技合作基地,贵州省先进医学成像与智能计算全省重点实验室,贵州省人民医院医学影像科,贵州 贵阳 550002贵州省精准影像诊疗国际科技合作基地,贵州省先进医学成像与智能计算全省重点实验室,贵州省人民医院医学影像科,贵州 贵阳 550002上海儿童医学中心贵州医院超声科,贵州 贵阳 550002贵州省精准影像诊疗国际科技合作基地,贵州省先进医学成像与智能计算全省重点实验室,贵州省人民医院医学影像科,贵州 贵阳 550002贵州省精准影像诊疗国际科技合作基地,贵州省先进医学成像与智能计算全省重点实验室,贵州省人民医院医学影像科,贵州 贵阳 550002贵州省精准影像诊疗国际科技合作基地,贵州省先进医学成像与智能计算全省重点实验室,贵州省人民医院医学影像科,贵州 贵阳 550002
医药卫生
血管畸形肺动脉计算机体层摄影血管造影术
Vascular MalformationsPulmonary ArteryComputed Tomography Angiography
《中国临床医学影像杂志》 2026 (9)
645-649,5
贵州省卫生健康高质量发展医学科研联合基金项目(2025GZYXKYJJXM0134)国家慢性病防治重大科技专项(2026ZD0557503)贵州省科技厅2026年临床专项(黔科合成果LC[2026]一般177).
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