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原发性颅内血管平滑肌瘤的MRI表现及误诊原因分析OA

MRI findings and misdiagnosis of primary intracranial angioleiomyoma

中文摘要英文摘要

目的:探讨原发性颅内血管平滑肌瘤(PIA)的MRI表现并分析其误诊原因.方法:回顾性分析3例PIA患者的临床及MRI资料.结果:3例均为颅内脑外的单发病灶,分别位于小脑幕下、海绵窦区和后颅窝.MRI上病灶主要表现为类圆形、分叶状或哑铃状实性肿块;T1WI呈稍低信号,T2WI及T2 FLAIR呈稍高信号;增强扫描2例呈明显均匀强化,1例呈不均匀明显强化;1例DWI呈低信号,ADC值为0.809×10-3 mm2/s;周围脑组织未见水肿.结论:PIA在MRI上表现为颅内脑外的实性肿块,边界清晰,明显强化,在颅内脑外病变的诊断中,需纳入此病作为鉴别诊断.

Objective:To investigate the MRI findings of primary intracranial angioleiomyoma(PIA)and analyze the causes of misdiagnosis.Methods:The clinical and MRI data of 3 PIA patients were retrospectively analyzed.Results:Three cases were solitary intracranial extracerebral lesions,located respectively in the subtentorial cerebellum,the cavernous sinus region and the posterior fossa.MRI mainly showed round,lobulated or dumbbell-shaped solid masses with slightly hypointensity on T1WI and slightly hyperintensity on T2WI and T2 FLAIR.Contrast-enhanced scans showed significant homogeneous enhancement in 2 cases and heterogeneous enhancement in 1 case.DWI revealed hypointensity in 1 case,with ADC value of 0.809×10-3 mm²/s.No edema was observed in the surrounding brain tissue.Conclusions:PIA lesion presents as a solid intracranial extracerebral mass with clear borders and significant enhancement on MRI.It should be included in the differential diagnosis of intracranial extracerebral lesions.

周兴顺;王宇军;马雯慧;贺鹏;俞祯妮;黄聪

联勤保障部队第九二六医院放射科,云南 开远 661699浙江中医药大学附属第一医院/浙江省中医院放射科,浙江 杭州 310006联勤保障部队第九二六医院放射科,云南 开远 661699广东三九脑科医院影像科,广东 广州 510510联勤保障部队第九二六医院放射科,云南 开远 661699联勤保障部队第九二六医院放射科,云南 开远 661699

医药卫生

原发性颅内血管平滑肌瘤磁共振成像误诊脑膜瘤神经鞘瘤孤立性纤维性肿瘤

Primary intracranial vascular leiomyomaMagnetic resonance imagingMisdiagnosisMeningiomaSchwannomaSolitary fibrous tumor

《中国中西医结合影像学杂志》 2026 (2)

244-247,4

联勤保障部队第九二六医院科技强院专项科研计划(926yy22xk14).

10.3969/j.issn.1672-0512.2026.02.023

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