Asymptomatic Ebstein''''s Anomaly in Children and Adults:Intervene or Observe?OA
Comments Ebstein''s Anomaly(EA)is a rare congenital heart disease(CHD)with an incidence of approximately 1 in 20,000.The pathognomonic feature involves apical displacement of the septal and posterior leaflets,resulting in valvular insufficiency and right ventricular(RV)remodeling.Untreated patients exhibit a cumulative mortality rate of up to 25% within the first decade,with heart failure(HF)and arrhythmias constituting the predominant causes of death.Current guidelines suggest that asymptomatic patients with accessory pathways may benefit from prophylactic ablation,though robust evidence specific to EA remains limited[1-3].
Runzhang Liang;Haiyun Yuan;Shusheng Wen
Department of Cardiovascular Surgery,Guangdong Provincial People''s Hospital(Guangdong Academy of Medical Sciences),Southern Medical University,Guangzhou,510080,China Department of Cardiovascular Surgery,Guangdong Cardiovascular Institute,Guangdong Provincial People''s Hospital,Guangdong Academy of Medical Sciences,Guangzhou,510080,ChinaDepartment of Cardiovascular Surgery,Guangdong Provincial People''s Hospital(Guangdong Academy of Medical Sciences),Southern Medical University,Guangzhou,510080,China Department of Cardiovascular Surgery,Guangdong Cardiovascular Institute,Guangdong Provincial People''s Hospital,Guangdong Academy of Medical Sciences,Guangzhou,510080,ChinaDepartment of Cardiovascular Surgery,Guangdong Provincial People''s Hospital(Guangdong Academy of Medical Sciences),Southern Medical University,Guangzhou,510080,China Department of Cardiovascular Surgery,Guangdong Cardiovascular Institute,Guangdong Provincial People''s Hospital,Guangdong Academy of Medical Sciences,Guangzhou,510080,China
医药卫生
congenital heart disease chdobservationapical displacement septal posterior leafletsresultingasymptomaticvalvular insufficiencyEbsteins anomalyinterventioncongenital heart disease
《Congenital Heart Disease》 2025 (4)
P.447-449,3
funded by E Fund Congenital Heart Disease Medical Talent Cultivation and Education Fund,grant number 2023QT0009the Science and Technology Planning Project of Guangdong Province,grant number 2023B03J1255.
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